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Creutzfeldt-Jakob Syndrome

"Creutzfeldt-Jakob Syndrome" is a descriptor in the National Library of Medicine's controlled vocabulary thesaurus, MeSH (Medical Subject Headings). Descriptors are arranged in a hierarchical structure, which enables searching at various levels of specificity.

expand / collapse MeSH information
A rare transmissible encephalopathy most prevalent between the ages of 50 and 70 years. Affected individuals may present with sleep disturbances, personality changes, ATAXIA; APHASIA, visual loss, weakness, muscle atrophy, MYOCLONUS, progressive dementia, and death within one year of disease onset. A familial form exhibiting autosomal dominant inheritance and a new variant CJD (potentially associated with ENCEPHALOPATHY, BOVINE SPONGIFORM) have been described. Pathological features include prominent cerebellar and cerebral cortical spongiform degeneration and the presence of PRIONS. (From N Engl J Med, 1998 Dec 31;339(27))


expand / collapse Publications
This graph shows the total number of publications written about "Creutzfeldt-Jakob Syndrome" by people in this website by year, and whether "Creutzfeldt-Jakob Syndrome" was a major or minor topic of these publications.
Below are the most recent publications written about "Creutzfeldt-Jakob Syndrome" by people in Profiles.
  1. Genome wide association study of clinical duration and age at onset of sporadic CJD. PLoS One. 2024; 19(7):e0304528.
    View in: PubMed
  2. Insufficient evidence for an association between iatrogenic Alzheimer's disease and cadaveric pituitary-derived growth hormone. Alzheimers Dement. 2024 Oct; 20(10):7399-7402.
    View in: PubMed
  3. Change in Epidemiology of Creutzfeldt-Jakob Disease in the US, 2007-2020. JAMA Neurol. 2024 Feb 01; 81(2):195-197.
    View in: PubMed
  4. PRNP expression predicts imaging findings in sporadic Creutzfeldt-Jakob disease. Ann Clin Transl Neurol. 2023 04; 10(4):536-552.
    View in: PubMed
  5. Right Brain: The Purple Scarf and the Cortical Ribbon. Neurology. 2023 03 14; 100(11):537-539.
    View in: PubMed
  6. Developing neuropalliative care for sporadic Creutzfeldt-Jakob Disease. Prion. 2022 12; 16(1):23-39.
    View in: PubMed
  7. Caregiver Experiences Navigating the Diagnostic Journey in a Rapidly Progressing Dementia. J Geriatr Psychiatry Neurol. 2023 07; 36(4):282-294.
    View in: PubMed
  8. Prions induce an early Arc response and a subsequent reduction in mGluR5 in the hippocampus. Neurobiol Dis. 2022 10 01; 172:105834.
    View in: PubMed
  9. Minimal change prion retinopathy: Morphometric comparison of retinal and brain prion deposits in Creutzfeldt-Jakob disease. Exp Eye Res. 2022 09; 222:109172.
    View in: PubMed
  10. Default Mode Network quantitative diffusion and resting-state functional magnetic resonance imaging correlates in sporadic Creutzfeldt-Jakob disease. Hum Brain Mapp. 2022 09; 43(13):4158-4173.
    View in: PubMed