13CValine metabolism in methylmalonicacidemia using nuclear magnetic resonance: propinonate as an obligate intermediate (Q35089675)

6 August 2017

title

13CValine metabolism in methylmalonicacidemia using nuclear magnetic resonance: propinonate as an obligate intermediate (English)

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17 August 2022

K. Tanaka

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17 August 2022

I. M. Armitage

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17 August 2022

H. S. Ramsdell

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17 August 2022

Y. E. Hsia

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17 August 2022

S. R. Lipsky

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17 August 2022

L. E. Rosenberg

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17 August 2022

language of work or name

English

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publication date

1 September 1975

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full work available at URL

6 August 2017

https://europepmc.org/articles/PMC433063

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https://europepmc.org/articles/PMC433063?pdf=render

17 August 2022

file format

Portable Document Format

online access status

open access

content deliverer

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https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A1059159

Proceedings of the National Academy of Sciences of the United States of America

17 August 2022

published in

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6 August 2017

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6 August 2017

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6 August 2017

page(s)

3692-3696

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THE METABOLISM OF PROPIONIC ACID.

6 August 2017

cites work

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=433063

Propionicacidemia, a New Inborn Error of Metabolism

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=433063

The conversion of valine to propionylcarnitine in isolated rat liver mitochondria

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=433063

Inherited propionyl-CoA carboxylase deficiency in “ketotic hyperglycinemia”

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=433063

Stable Isotope Tracers in the Life Sciences and Medicine

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=433063

Carbon-13 as a Label in Biosynthetic Studies

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=433063

3-Hydroxypropionate: Significance of β-Oxidation of Propionate in Patients with Propionic Acidemia and Methylmalonic Acidemia

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=433063

Properties of purified methylmalonate semialdehyde dehydrogenase of Pseudomonas aeruginosa.

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=433063

Oxidation of methylmalonate semialdehyde to propionyl coenzyme A in Pseudomonas aeruginosa grown on valine

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=433063

Nuclear magnetic resonance spectroscopy: reinvestigation of carbon-13 spin-lattice relaxation time measurements of amino acids

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=433063

Methylmalonic aciduria. An inborn error leading to metabolic acidosis, long-chain ketonuria and intermittent hyperglycinemia

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=433063

Metabolism of Propionic Acid in Animal Tissues

27 September 2018

1 reference

12 December 2020

Enzymatic synthesis of branched chain acids from amino acids

1 reference

12 December 2020

Coenzyme A thiol esters of isobutyric, methacrylic, and beta-hydroxyisobutyric acids as intermediates in the enzymatic degradation of valine

1 reference

12 December 2020

Isotope studies on the metabolism of valine

1 reference

12 December 2020

Defective metabolism of vitamin B12 in fibroblasts from children with methylmalonicaciduria

1 reference

12 December 2020

Identifiers

DOI

10.1073/PNAS.72.9.3692

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6 August 2017

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6 August 2017

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