Estrogen protection in Friedreich's ataxia skin fibroblasts (Q35046921)

6 August 2017

title

Estrogen protection in Friedreich's ataxia skin fibroblasts (English)

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6 August 2017

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Timothy E Richardson

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6 August 2017

Shao-Hua Yang

series ordinal

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6 August 2017

Yi Wen

series ordinal

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6 August 2017

James W Simpkins

series ordinal

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6 August 2017

language of work or name

English

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publication date

3 May 2011

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6 August 2017

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6 August 2017

volume

152

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6 August 2017

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6 August 2017

page(s)

2742-2749

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Friedreich's ataxia induced pluripotent stem cells model intergenerational GAA⋅TTC triplet repeat instability

6 August 2017

cites work

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8 July 2018

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Loss of estrogen receptor beta decreases mitochondrial energetic potential and increases thrombogenicity of platelets in aged female mice

8 July 2018

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Role of protein phosphatases and mitochondria in the neuroprotective effects of estrogens

8 July 2018

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Diagnosis and treatment of Friedreich ataxia: a European perspective

8 July 2018

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Estrogens directly potentiate neuronal L-type Ca2+ channels

8 July 2018

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Estrogen actions on mitochondria--physiological and pathological implications

8 July 2018

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Iron-dependent regulation of frataxin expression: implications for treatment of Friedreich ataxia

8 July 2018

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Mechanistic investigations on the antioxidant action of a neuroprotective estrogen derivative

8 July 2018

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Protective effects of Fe-Aox29, a novel antioxidant derived from a molecular combination of Idebenone and vitamin E, in immortalized fibroblasts and fibroblasts from patients with Friedreich Ataxia.

8 July 2018

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8 July 2018

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GAA repeat expansion mutation mouse models of Friedreich ataxia exhibit oxidative stress leading to progressive neuronal and cardiac pathology

8 July 2018

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Friedreich's ataxia: from disease mechanisms to therapeutic interventions

8 July 2018

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Development of 17alpha-estradiol as a neuroprotective therapeutic agent: rationale and results from a phase I clinical study

8 July 2018

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Quinol-based cyclic antioxidant mechanism in estrogen neuroprotection

8 July 2018

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Oxidative Damage to Human Lens Epithelial Cells in Culture: Estrogen Protection of Mitochondrial Potential, ATP, and Cell Viability

8 July 2018

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A cellular model for Friedreich Ataxia reveals small-molecule glutathione peroxidase mimetics as novel treatment strategy

8 July 2018

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Aconitase and mitochondrial iron-sulphur protein deficiency in Friedreich ataxia

8 July 2018

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The Friedreich ataxia GAA triplet repeat: premutation and normal alleles.

8 July 2018

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Regulation of mitochondrial iron accumulation by Yfh1p, a putative homolog of frataxin

8 July 2018

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Clinical and genetic abnormalities in patients with Friedreich's ataxia

8 July 2018

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Friedreich's ataxia: autosomal recessive disease caused by an intronic GAA triplet repeat expansion

8 July 2018

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Comparison between novel steroid-like and conventional nonsteroidal antioestrogens in inhibiting oestradiol- and IGF-I-induced proliferation of human breast cancer-derived cells

8 July 2018

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17-beta estradiol protects neurons from oxidative stress-induced cell death in vitro

8 July 2018

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Classification of the hereditary ataxias and paraplegias

8 July 2018

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Friedreich's ataxia: a descriptive epidemiological study in an Italian population

8 July 2018

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Estrogen receptor-independent neuroprotection via protein phosphatase preservation and attenuation of persistent extracellular signal-regulated kinase 1/2 activation

8 July 2018

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Mitochondria-targeted antioxidants protect Friedreich Ataxia fibroblasts from endogenous oxidative stress more effectively than untargeted antioxidants.

25 October 2018

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Estradiol protects against ATP depletion, mitochondrial membrane potential decline and the generation of reactive oxygen species induced by 3-nitroproprionic acid in SK-N-SH human neuroblastoma cells

25 October 2018

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Abnormalities of mitochondrial enzymes in Alzheimer disease

25 October 2018

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Estrogens may reduce mortality and ischemic damage caused by middle cerebral artery occlusion in the female rat.

25 October 2018

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Estrogen protects primary cortical neurons from glutamate toxicity

25 October 2018

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Estradiol treatment increases viability of glioma and neuroblastoma cells in vitro.

25 October 2018

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Clinical, biochemical and molecular genetic correlations in Friedreich's ataxia

25 October 2018

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12 December 2020

Human cultured skin fibroblasts express estrogen receptor alpha and beta

1 reference

12 December 2020

Mitochondrial mechanisms of estrogen neuroprotection

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12 December 2020

Clinical Description and Roentgenologic Evaluation of Patients with Friedreich's Ataxia

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12 December 2020

Friedreich's ataxia: a clinical and genetic study of 90 families with an analysis of early diagnostic criteria and intrafamilial clustering of clinical features

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12 December 2020

Deficiencies in complex I subunits of the respiratory chain in Parkinson's disease

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12 December 2020

Abnormalities of the electron transport chain in idiopathic Parkinson's disease

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12 December 2020

Estrogens attenuate and corticosterone exacerbates excitotoxicity, oxidative injury, and amyloid beta-peptide toxicity in hippocampal neurons

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12 December 2020

Correlation between left ventricular hypertrophy and GAA trinucleotide repeat length in Friedreich's ataxia

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12 December 2020

Molecular genetics and pathogenesis of Friedreich ataxia

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12 December 2020

Echocardiographic characterization of cardiomyopathy in Friedreich's ataxia with tissue Doppler echocardiographically derived myocardial velocity gradients

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12 December 2020

Identifiers

DOI

10.1210/EN.2011-0184

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6 August 2017

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6 August 2017

1 reference