Endocardial Fibroelastosis
"Endocardial Fibroelastosis" is a descriptor in the National Library of Medicine's controlled vocabulary thesaurus,
MeSH (Medical Subject Headings). Descriptors are arranged in a hierarchical structure,
which enables searching at various levels of specificity.
A condition characterized by the thickening of ENDOCARDIUM due to proliferation of fibrous and elastic tissue, usually in the left ventricle leading to impaired cardiac function (CARDIOMYOPATHY, RESTRICTIVE). It is most commonly seen in young children and rarely in adults. It is often associated with congenital heart anomalies (HEART DEFECTS CONGENITAL;) INFECTION; or gene mutation. Defects in the tafazzin protein, encoded by TAZ gene, result in a form of autosomal dominant familial endocardial fibroelastosis.
| Descriptor ID |
D004695
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| MeSH Number(s) |
C14.280.238.281
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| Concept/Terms |
Endocardial Fibroelastosis- Endocardial Fibroelastosis
- Endocardial Fibroelastoses
- Fibroelastoses, Endocardial
- Fibroelastosis, Endocardial
- Endomyocardial Fibroelastosis
|
Below are MeSH descriptors whose meaning is more general than "Endocardial Fibroelastosis".
Below are MeSH descriptors whose meaning is more specific than "Endocardial Fibroelastosis".
This graph shows the total number of publications written about "Endocardial Fibroelastosis" by people in this website by year, and whether "Endocardial Fibroelastosis" was a major or minor topic of these publications.
Below are the most recent publications written about "Endocardial Fibroelastosis" by people in Profiles.
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Patterns of endocardial fibroelastosis without atrioventricular block in fetuses exposed to anti-Ro/SSA antibodies. Ultrasound Obstet Gynecol. 2023 07; 62(1):148-151.
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Outcome of Antibody-Mediated Fetal Heart Disease With Standardized Anti-Inflammatory Transplacental Treatment. J Am Heart Assoc. 2022 02; 11(3):e023000.
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Recessive ciliopathy mutations in primary endocardial fibroelastosis: a rare neonatal cardiomyopathy in a case of Alstrom syndrome. J Mol Med (Berl). 2021 11; 99(11):1623-1638.
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Primary endocardial fibroelastosis: an underappreciated cause of cardiomyopathy in children. Cardiovasc Pathol. 2013 Sep-Oct; 22(5):345-50.
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Use of intravenous gamma globulin and corticosteroids in the treatment of maternal autoantibody-mediated cardiomyopathy. J Am Coll Cardiol. 2011 Feb 08; 57(6):715-23.
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Ross-Konno and endocardial fibroelastosis resection after hybrid stage I palliation in infancy: successful staged left-ventricular rehabilitation and conversion to biventricular circulation after fetal diagnosis of aortic stenosis. Pediatr Cardiol. 2011 Feb; 32(2):211-4.
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Maternal anti-Ro and anti-La antibody-associated endocardial fibroelastosis. Circulation. 2002 Feb 19; 105(7):843-8.
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Cardiac transplantation in children and adolescents. Circulation. 1987 Nov; 76(5 Pt 2):V43-7.
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Yield of endomyocardial biopsy in patients with biventricular failure. Comparison of patients with normal vs reduced left ventricular ejection fraction. Chest. 1986 Aug; 90(2):181-4.
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Three cases of idiopathic cardiomegaly in the aged, with special references to the morphological specificity and to the conduction system. Jpn Heart J. 1971 May; 12(3):305-15.