(Q34347066)

1 August 2017

title

Expression of abnormal von Willebrand factor by endothelial cells from a patient with type IIA von Willebrand disease (English)

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1 August 2017

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R B Levene

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1 August 2017

F M Booyse

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1 August 2017

J Chediak

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1 August 2017

T S Zimmerman

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1 August 2017

D M Livingston

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1 August 2017

D C Lynch

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1 August 2017

language of work or name

English

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publication date

1 September 1987

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Proceedings of the National Academy of Sciences of the United States of America

1 August 2017

published in

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1 August 2017

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1 August 2017

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1 August 2017

page(s)

6550-6554

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Serial propagation of human endothelial cells in vitro

1 August 2017

cites work

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https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=299116

Isolation and characterization of full-length cDNA clones for human alpha-, beta-, and gamma-actin mRNAs: skeletal but not cytoplasmic actins have an amino-terminal cysteine that is subsequently removed

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=299116

Immunolocalization of von Willebrand protein in Weibel-Palade bodies of human endothelial cells

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=299116

Factor VIII/von Willebrand factor.

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=299116

Biosynthesis of von Willebrand protein by human endothelial cells: processing steps and their intracellular localization

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=299116

Inhibition of disulfide bonding of von Willebrand protein by monensin results in small, functionally defective multimers

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=299116

Molecular cloning of cDNA for human von Willebrand factor: authentication by a new method

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=299116

An explanation for minor multimer species in endothelial cell-synthesized von Willebrand factor

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=299116

Subunit composition of plasma von Willebrand factor. Cleavage is present in normal individuals, increased in IIA and IIB von Willebrand disease, but minimal in variants with aberrant structure of individual oligomers (types IIC, IID, and IIE).

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=299116

Transplantation of normal bone marrow into a pig with severe von Willebrand's disease

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=299116

Inducible secretion of large, biologically potent von Willebrand factor multimers

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=299116

Initial glycosylation and acidic pH in the Golgi apparatus are required for multimerization of von Willebrand factor

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=299116

In vitro correction of the abnormal multimeric structure of von Willebrand factor in type IIa von Willebrand's disease

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=299116

Epitope mapping of the von Willebrand factor subunit distinguishes fragments present in normal and type IIA von Willebrand disease from those generated by plasmin

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=299116

Characterization and properties of cultured human von Willebrand umbilical vein endothelial cells

6 July 2018

1 reference

12 December 2020

Multimeric composition of factor VIII/von Willebrand factor following administration of DDAVP: implications for pathophysiology and therapy of von Willebrand's disease subtypes

1 reference

12 December 2020

Biosynthesis of von Willebrand protein by human endothelial cells. Identification of a large precursor polypeptide chain

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12 December 2020

Subunit composition of oligomeric human von Willebrand factor

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12 December 2020

Human endothelial cells: use of heparin in cloning and long-term serial cultivation

1 reference

12 December 2020

The heterogeneity of type IIA von Willebrand's disease: studies with protease inhibitors

1 reference

12 December 2020

Identifiers

DOI

10.1073/PNAS.84.18.6550

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1 August 2017

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1 August 2017

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